ABOUT IPF

WHAT IS IDIOPATHIC PULMONARY FIBROSIS (IPF)?

IPF is a specific type of pulmonary fibrosis in which the small air sacs of the lung, known as "alveoli" (see Figure 1), gradually become replaced by fibrotic (scar) tissue. The scarring begins in the tissue between the air sacs. Normally, this tissue is a thin layer consisting of a few cells. But scarring with IPF causes the tissue to thicken and become stiff, preventing oxygen from getting into the bloodstream. Over time, the scarring of the lung gets worse, the lungs become stiff, and breathing becomes more difficult. You may find yourself increasingly short of breath.

HOW DOES IPF PROGRESS?

It is important to realize that IPF progresses differently in each patient. For some, the scarring occurs quickly, while in others it happens over a longer period of time. Symptoms also vary from moderate to severe and may stay the same for awhile. Because of the differences from patient to patient, you may find it helpful to discuss the progress of your disease with your physician.

Related Links: Causes of IPF, Signs & Symptoms, Diagnosis, Therapies

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